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dihydrolipoamide acyltransferase MeSH Supplementary Concept Data 2025


MeSH Supplementary
dihydrolipoamide acyltransferase
Unique ID
C033588
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/C033588
Entry Term(s)
BCOADC-E2
E2 transacylase
branched chain acyltransferase
dihydrolipoyl transacylase
Registry Numbers
EC 2.3.1.-
Heading Mapped to
*Acyltransferases
Frequency
64
Note
component of branched-chain 2-oxo acid dehydrogenase multienzyme complex; mutation in this (E2) catalytic subunit identifies type II maple syrup urine disease; do not confuse with E2 enzymes of pyruvate dehydrogenase (PDC) and alpha-ketoglutarate dehydrogenase complexes
Source
Biochem J 1981;200(1):59
Date of Entry
1982/03/12
Revision Date
2001/01/12
dihydrolipoamide acyltransferase Preferred
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