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2-hydroxyacid dehydrogenase MeSH Supplementary Concept Data 2025


MeSH Supplementary
2-hydroxyacid dehydrogenase
Unique ID
C083779
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/C083779
Entry Term(s)
2-hydroxyglutaric acid dehydrogenase (NAD)
L-2-hydroxyacid dehydrogenase
Registry Numbers
EC 1.1.1.-
Heading Mapped to
*Alcohol Oxidoreductases
Frequency
26
Note
requires NAD+; deficiency creates L-2-hydroxyglutaric acidemia; do not confuse with EC 1.1.3.15 which uses O2 or EC 1.1.99.2 which uses an unspecified acceptor
Source
J Inherit Metab Dis 1993;16(4):753-61
Date of Entry
1993/11/19
Revision Date
2001/01/29
2-hydroxyacid dehydrogenase Preferred
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