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4a-hydroxy-erythro-5,6,7,8-tetrahydrobiopterin dehydratase MeSH Supplementary Concept Data 2025


MeSH Supplementary
4a-hydroxy-erythro-5,6,7,8-tetrahydrobiopterin dehydratase
Unique ID
C114534
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/C114534
Entry Term(s)
4a-OH-6BH4-dehydratase
4a-hydroxy-6BH4-dehydratase
Registry Numbers
EC 4.2.1.-
Heading Mapped to
*Hydro-Lyases
Frequency
3
Note
converts (6R)-L-erythro-5,6,7,8-tetrahydrobiopterin to quinoid dihydropterin; defect in Hermansky-Pudlak syndromeresults in decreased levels of biopterin
Source
J Invest Dermatol 1998 Sep;111(3):511-6
Date of Entry
1998/10/01
Revision Date
2001/03/28
4a-hydroxy-erythro-5,6,7,8-tetrahydrobiopterin dehydratase Preferred
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