MeSH Browser

MeSH Supplementary: 2-methyl-3-hydroxybutyryl-coenzyme A dehydrogenase
Unique ID: C419903
RDF Unique Identifier: http://id.nlm.nih.gov/mesh/C419903
Entry Term(s): (2S,3S)-3-hydroxy-2-methylbutanoyl-CoA + NAD+ - oxidoreductase; 2-MHB-CoA dehydrogenase; 2-methyl-3-hydroxybutyryl-CoA dehydrogenase
Registry Numbers: EC 1.1.1.178
Heading Mapped to: *3-Hydroxyacyl CoA Dehydrogenases
Frequency: 14
Note: reaction:(2S,3S)-3-hydroxy-2-methylbutanoyl-CoA + NAD+ = 2-methylacetoacetyl-CoA + NADH; deficiency is associated with progressive infantile neurodegeneration
Source: Pediatr Res. 2000 Dec;48(6):852-5
Date of Entry: 2001/02/14
Revision Date: 2015/03/02

2-methyl-3-hydroxybutyryl-coenzyme A dehydrogenase MeSH Supplementary Concept Data 2025