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Kaposiform Hemangioendothelioma MeSH Supplementary Concept Data 2022


MeSH Supplementary
Kaposiform Hemangioendothelioma
Unique ID
C537007
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/C537007
Entry Term(s)
Congenital cutaneous multifocal kaposiform hemangioendothelioma
Kaposiform hemangio-endothelioma
Registry Number
0
Heading Mapped to
*Hemangioendothelioma
*Sarcoma, Kaposi
*Kasabach-Merritt Syndrome
Frequency
181
Note
A rare, locally aggressive vascular neoplasm that primarily occurs in childhood. It originates on the skin and is characterized by one or multiple masse; it is often comorbid with Kasabach-Merritt syndrome and lymphangiomatosis. The viscera is usually not affected, but invasion of bone, retroperitoneum, and MEDIASTINUM has occured in some cases. No metastases have been reported.
Date of Entry
2010/08/25
Revision Date
2016/07/19
Kaposiform Hemangioendothelioma Preferred
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