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Lymphangiectasia, pulmonary, congenital MeSH Supplementary Concept Data 2025


MeSH Supplementary
Lymphangiectasia, pulmonary, congenital
Unique ID
C537727
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/C537727
Entry Term(s)
Lymphangiectasia pulmonary congenital
Lymphangiomatosis, pulmonary
Pulmonary cystic lymphangiectasis
Registry Numbers
0
Heading Mapped to
Lung Diseases / congenital
Lymphangiectasis / congenital
Frequency
69
Note
A hereditary form of lymphangiectasis that affects the lungs and is frequently lethal in utero. It is characterized by chronic pleural effusions, pachypleuritis, pleural membrane thickenings, EDEMA; HYDROPS FETALIS, growth retardation, and recurrent RESPIRATORY INFECTIONS. OMIM: 265300
Date of Entry
2010/08/25
Revision Date
2015/08/18
Lymphangiectasia, pulmonary, congenital Preferred
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