MeSH Browser

MeSH Supplementary: Lymphangiectasia, pulmonary, congenital
Unique ID: C537727
RDF Unique Identifier: http://id.nlm.nih.gov/mesh/C537727
Entry Term(s): Lymphangiectasia pulmonary congenital; Lymphangiomatosis, pulmonary; Pulmonary cystic lymphangiectasis
Registry Numbers: 0
Heading Mapped to: Lung Diseases / congenital; Lymphangiectasis / congenital
Frequency: 69
Note: A hereditary form of lymphangiectasis that affects the lungs and is frequently lethal in utero. It is characterized by chronic pleural effusions, pachypleuritis, pleural membrane thickenings, EDEMA; HYDROPS FETALIS, growth retardation, and recurrent RESPIRATORY INFECTIONS. OMIM: 265300
Date of Entry: 2010/08/25
Revision Date: 2015/08/18

Lymphangiectasia, pulmonary, congenital MeSH Supplementary Concept Data 2025