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Progressive Encephalomyelitis with Rigidity MeSH Supplementary Concept Data 2025


MeSH Supplementary
Progressive Encephalomyelitis with Rigidity
Unique ID
C566113
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/C566113
Registry Numbers
0
Heading Mapped to
*Encephalomyelitis
*Muscle Rigidity
Frequency
37
Note
An acquired sporadic disorder with similar findings to STIFF-PERSON SYNDROME (OMIM: 184850) but also characterized by encephalomyelitis and additional autonomic findings such as generalized HYPERHIDROSIS; TACHYCARDIA; HYPERTHERMIA and HYPERTENSION, as well as increased sensitivity to external stimuli.
Date of Entry
2012/11/05
Revision Date
2015/09/27
Progressive Encephalomyelitis with Rigidity Preferred
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