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Carbamoyl-Phosphate Synthase (Ammonia) MeSH Descriptor Data 2025


MeSH Heading
Carbamoyl-Phosphate Synthase (Ammonia)
Tree Number(s)
D08.811.464.259.350
Unique ID
D002222
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D002222
Annotation
/defic: consider CARBAMOYL-PHOSPHATE SYNTHETASE I DEFICIENCY DISEASE
Scope Note
An enzyme that catalyzes the formation of carbamoyl phosphate from ATP, carbon dioxide, and ammonia. This enzyme is specific for arginine biosynthesis or the urea cycle. Absence or lack of this enzyme may cause CARBAMOYL-PHOSPHATE SYNTHASE I DEFICIENCY DISEASE. EC 6.3.4.16.
Entry Version
AMMONIA CP SYNTHASE
Entry Term(s)
CP Synthase I
Carbamoyl Phosphate Synthetase I
Carbamoyl-Phosphate Synthetase (Ammonia)
Carbamoyl-Phosphate Synthetase I
Carbamoylphosphate Synthetase I
Carbamyl Phosphate Synthase (Ammonia)
Carbamyl-Phosphate Synthase (Ammonia)
Registry Numbers
EC 6.3.4.16
Related Numbers
9026-23-7
CAS Type 1 Name
Carbon dioxide:ammonia ligase (ADP-forming, carbamate-phosphorylating)
Previous Indexing
Ammonia (1974)
Carbamates (1974)
Phosphotransferases, ATP (1974)
See Also
Carbamoyl-Phosphate Synthase I Deficiency Disease
Public MeSH Note
98; see CARBAMYL PHOSPHATE SYNTHASE (AMMONIA) 1989-97; see LIGASES 1981-88; see PHOSPHOTRANSFERASES, ATP 1975-80
History Note
98(75)
Date Established
1989/01/01
Date of Entry
1974/11/19
Revision Date
2016/06/28
Carbamoyl-Phosphate Synthase (Ammonia) Preferred
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