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Hamman-Rich Syndrome MeSH Descriptor Data 2024


MeSH Heading
Hamman-Rich Syndrome
Tree Number(s)
C08.381.483.652.500.500
Unique ID
D000080203
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D000080203
Scope Note
Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.
Entry Term(s)
Acute Interstitial Pneumonia
Acute Interstitial Pneumonitis
Hamman-Rich Disease
Public MeSH Note
for HAMMAN-RICH SYNDROME see PULMONARY FIBROSIS 1984-2019; for HAMMAN-RICH SYNDROME see IDIOPATHIC PULMONARY FIBROSIS 2010-2019
History Note
2020; for HAMMAN-RICH SYNDROME use PULMONARY FIBROSIS 1984-2019; for HAMMAN-RICH SYNDROME use IDIOPATHIC PULMONARY FIBROSIS 2010-2019
Date Established
2020/01/01
Date of Entry
2019/07/08
Revision Date
2021/05/10
Hamman-Rich Syndrome Preferred
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