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Glycogen Debranching Enzyme System MeSH Descriptor Data 2022


MeSH Heading
Glycogen Debranching Enzyme System
Tree Number(s)
D08.811.277.450.420.450
D08.811.913.400.450.460.350
Unique ID
D006004
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D006004
Annotation
/defic: consider also GLYCOGEN STORAGE DISEASE TYPE III
Scope Note
1,4-alpha-D-Glucan-1,4-alpha-D-glucan 4-alpha-D-glucosyltransferase/dextrin 6 alpha-D-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (EC 2.4.1.25) and amylo-1,6-glucosidase (EC 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-D-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-D-glucan. As a glucosidase it catalyzes the endohydrolysis of 1,6-alpha-D-glucoside linkages at points of branching in chains of 1,4-linked alpha-D-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III.
Entry Term(s)
Glycogen Debranching Enzyme
Transfer-Glucosidase
Registry Number
0
Previous Indexing
Glucosidase (1973-1975)
Glucosyltransferases (1973-1975)
Glycogen (1973-1975)
See Also
Glycogen Storage Disease Type III
Public MeSH Note
89; was GLYCOGEN DEBRANCHING ENZYME see under GLUCOSYLTRANSFERASES 1976-88
Online Note
use GLYCOGEN DEBRANCHING ENZYME SYSTEM to search GLYCOGEN DEBRANCHING ENZYME 1976-88
History Note
89(76); was GLYCOGEN DEBRANCHING ENZYME see under GLUCOSYLTRANSFERASES 1976-88
Date Established
1989/01/01
Date of Entry
1975/07/21
Revision Date
2003/07/09
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