- Concept UI
- M0368823
- Scope Note
- The 46,XX gonadal dysgenesis may be sporadic or familial. Familial XX gonadal dysgenesis is transmitted as an autosomal recessive trait and its locus was mapped to chromosome 2. Mutation in the gene for the FSH receptor (RECEPTORS, FSH) was detected. Sporadic XX gonadal dysgenesis is heterogeneous and has been associated with trisomy-13 and trisomy-18. These phenotypic females are characterized by a normal stature, sexual infantilism, bilateral streak gonads, amenorrhea, elevated plasma LUTEINIZING HORMONE and FSH concentration.
- Terms
-
Gonadal Dysgenesis, 46,XX
Preferred Term
Term UI
T423027
Date08/31/2000
LexicalTag
NON
ThesaurusID
NLM (2002)
-
Gonadal Dysgenesis, XX Type
Term UI
T765153
Date02/01/2010
LexicalTag
NON
ThesaurusID
-
Gonadal Dysgenesis, 46, XX
Term UI
T765847
Date02/17/2010
LexicalTag
NON
ThesaurusID
NLM (2011)