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Erdheim-Chester Disease MeSH Descriptor Data 2025


MeSH Heading
Erdheim-Chester Disease
Tree Number(s)
C15.604.250.410.224
Unique ID
D031249
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D031249
Scope Note
A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones.
Entry Term(s)
Granulomatosis, Lipid
Previous Indexing
Histiocytosis (1989-2002)
Histiocytosis, Langerhans-Cell (1988-2002)
Histiocytosis, Non-Langerhans-Cell (1991-2002)
Lipidosis (1979-2002)
Xanthomatosis (1979-2002)
Public MeSH Note
2003
History Note
2003
Date Established
2003/01/01
Date of Entry
2002/07/03
Revision Date
2008/07/08
Erdheim-Chester Disease Preferred
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