MeSH Browser

MeSH Heading: Arnold-Chiari Malformation
Tree Number(s): C10.500.680.291; C16.131.666.680.291
Unique ID: D001139
RDF Unique Identifier: http://id.nlm.nih.gov/mesh/D001139
Annotation: do not confuse with CHIARI'S SYNDROME see BUDD-CHIARI SYNDROME
Scope Note: A group of congenital malformations involving the brainstem, cerebellum, upper spinal cord, and surrounding bony structures. Type II is the most common, and features compression of the medulla and cerebellar tonsils into the upper cervical spinal canal and an associated MENINGOMYELOCELE. Type I features similar, but less severe malformations and is without an associated meningomyelocele. Type III has the features of type II with an additional herniation of the entire cerebellum through the bony defect involving the foramen magnum, forming an ENCEPHALOCELE. Type IV is a form a cerebellar hypoplasia. Clinical manifestations of types I-III include TORTICOLLIS; opisthotonus; HEADACHE; VERTIGO; VOCAL CORD PARALYSIS; APNEA; NYSTAGMUS, CONGENITAL; swallowing difficulties; and ATAXIA. (From Menkes, Textbook of Child Neurology, 5th ed, p261; Davis, Textbook of Neuropathology, 2nd ed, pp236-46)
Entry Term(s): Arnold-Chiari Deformity; Arnold-Chiari Malformation, Type 1; Arnold-Chiari Malformation, Type 2; Arnold-Chiari Malformation, Type 3; Arnold-Chiari Malformation, Type 4; Arnold-Chiari Malformation, Type I; Arnold-Chiari Malformation, Type II; Arnold-Chiari Malformation, Type III; Arnold-Chiari Malformation, Type IV; Arnold-Chiari Syndrome; Chiari Malformation Type 2; Chiari Malformation Type I; Chiari Malformation Type II; Malformation, Arnold-Chiari; Type I Arnold-Chiari Malformation; Type II Arnold-Chiari Malformation; Type III Arnold-Chiari Malformation; Type IV Arnold-Chiari Malformation
NLM Classification #: WL 101
Public MeSH Note: 2000; see ARNOLD-CHIARI DEFORMITY 1963-1999; for ARNOLD-CHIARI MALFORMATION see ARNOLD-CHIARI DEFORMITY 1963-1999
History Note: 2000(1963)
Date Established: 1966/01/01
Date of Entry: 1999/01/01
Revision Date: 2014/06/13

Allowable Qualifiers: blood (BL)

cerebrospinal fluid (CF)

chemically induced (CI)

classification (CL)

complications (CO)

diagnosis (DI)

diagnostic imaging (DG)

diet therapy (DH)

drug therapy (DT)

economics (EC)

embryology (EM)

enzymology (EN)

epidemiology (EP)

ethnology (EH)

etiology (ET)

genetics (GE)

history (HI)

immunology (IM)

metabolism (ME)

microbiology (MI)

mortality (MO)

nursing (NU)

parasitology (PS)

pathology (PA)

physiopathology (PP)

prevention & control (PC)

psychology (PX)

radiotherapy (RT)

rehabilitation (RH)

surgery (SU)

therapy (TH)

urine (UR)

veterinary (VE)

virology (VI)

Nervous System Diseases [C10]
- Nervous System Malformations [C10.500]
  - Neural Tube Defects [C10.500.680]

Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16]
- Congenital Abnormalities [C16.131]
  - Nervous System Malformations [C16.131.666]
    - Neural Tube Defects [C16.131.666.680]

Arnold-Chiari Malformation Preferred

Concept UI: M0001704
Scope Note: A group of congenital malformations involving the brainstem, cerebellum, upper spinal cord, and surrounding bony structures. Type II is the most common, and features compression of the medulla and cerebellar tonsils into the upper cervical spinal canal and an associated MENINGOMYELOCELE. Type I features similar, but less severe malformations and is without an associated meningomyelocele. Type III has the features of type II with an additional herniation of the entire cerebellum through the bony defect involving the foramen magnum, forming an ENCEPHALOCELE. Type IV is a form a cerebellar hypoplasia. Clinical manifestations of types I-III include TORTICOLLIS; opisthotonus; HEADACHE; VERTIGO; VOCAL CORD PARALYSIS; APNEA; NYSTAGMUS, CONGENITAL; swallowing difficulties; and ATAXIA. (From Menkes, Textbook of Child Neurology, 5th ed, p261; Davis, Textbook of Neuropathology, 2nd ed, pp236-46)
Terms: Arnold-Chiari Malformation Preferred Term
Term UI T365662
Date11/04/1999
LexicalTag EPO
ThesaurusID; Arnold-Chiari Deformity
Term UI T003424
Date01/01/1999
LexicalTag EPO
ThesaurusID NLM (1966); Arnold-Chiari Syndrome
Term UI T003425
Date12/28/1989
LexicalTag EPO
ThesaurusID NLM (1991); Malformation, Arnold-Chiari
Term UI T372011
Date11/04/1999
LexicalTag EPO
ThesaurusID NLM (2000)

Arnold-Chiari Malformation, Type I Narrower

Arnold-Chiari Malformation, Type II Narrower

Arnold-Chiari Malformation, Type III Narrower

Arnold-Chiari Malformation, Type IV Narrower

Arnold-Chiari Malformation MeSH Descriptor Data 2024