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Hirschsprung Disease MeSH Descriptor Data 2024


MeSH Heading
Hirschsprung Disease
Tree Number(s)
C06.198.439
C06.405.469.158.701.439
C16.131.314.439
Unique ID
D006627
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D006627
Annotation
acquired megacolon = MEGACOLON
Scope Note
Congenital MEGACOLON resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the LARGE INTESTINE. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the RECTUM and SIGMOID COLON.
Entry Version
HIRSCHSPRUNG DIS
Entry Term(s)
Aganglionic Megacolon
Aganglionosis, Colonic
Aganglionosis, Rectosigmoid Colon
Aganglionosis, Total Colonic
Colonic Aganglionosis
Congenital Intestinal Aganglionosis
Congenital Megacolon
Hirschsprung's Disease
Megacolon, Aganglionic
Megacolon, Congenital
Rectosigmoid Aganglionosis
Total Colonic Aganglionosis
NLM Classification #
WI 528
Previous Indexing
Megacolon (1966-1982)
Public MeSH Note
83; was HIRSCHSPRUNG'S DISEASE see MEGACOLON 1963-82
Online Note
search MEGACOLON 1966-82
History Note
83; was HIRSCHSPRUNG'S DISEASE see MEGACOLON 1963-82
Date Established
1983/01/01
Date of Entry
1982/04/27
Revision Date
2013/07/08
Hirschsprung Disease Preferred
Aganglionosis, Rectosigmoid Colon Narrower
Congenital Intestinal Aganglionosis Narrower
Aganglionosis, Colonic Narrower
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