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Pseudohypoaldosteronism MeSH Descriptor Data 2025


MeSH Heading
Pseudohypoaldosteronism
Tree Number(s)
C12.050.351.968.419.815.770
C12.200.777.419.815.770
C12.950.419.815.770
C16.320.831.770
Unique ID
D011546
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D011546
Scope Note
A heterogeneous group of disorders characterized by renal electrolyte transport dysfunctions. Congenital forms are rare autosomal disorders characterized by neonatal hypertension, HYPERKALEMIA, increased RENIN activity and ALDOSTERONE concentration. The Type I features HYPERKALEMIA with sodium wasting; Type II, HYPERKALEMIA without sodium wasting. Pseudohypoaldosteronism can be the result of a defective renal electrolyte transport protein or acquired after KIDNEY TRANSPLANTATION.
Entry Term(s)
Familial Hyperpotassemia and Hypertension
Familial Hypertensive Hyperkalemia
Gordon Hyperkalemia-Hypertension Syndrome
Hyperpotassemia and Hypertension, Familial
Hypertensive Hyperkalemia, Familial
Pseudohypoaldosteronism Type 1
Pseudohypoaldosteronism Type 1, Autosomal Dominant
Pseudohypoaldosteronism Type 1, Autosomal Recessive
Pseudohypoaldosteronism Type 2
Pseudohypoaldosteronism Type I
Pseudohypoaldosteronism Type II
Pseudohypoaldosteronism, Type I
Pseudohypoaldosteronism, Type I, Autosomal Dominant
Pseudohypoaldosteronism, Type I, Autosomal Recessive
Pseudohypoaldosteronism, Type II
Previous Indexing
Aldosterone (1971-1987)
Hyperaldosteronism (1975-1980)
Renal Tubular Transport, Inborn Errors (1971-1987)
See Also
Epithelial Sodium Channels
Receptors, Mineralocorticoid
Public MeSH Note
1991; see RENAL TUBULAR TRANSPORT, INBORN ERRORS 1988-90
History Note
1991(1988); use RENAL TUBULAR TRANSPORT, INBORN ERRORS 1988-90
Date Established
1991/01/01
Date of Entry
1987/03/13
Revision Date
2021/06/30
Pseudohypoaldosteronism Preferred
Pseudohypoaldosteronism, Type I, Autosomal Dominant Narrower
Pseudohypoaldosteronism, Type I, Autosomal Recessive Narrower
Pseudohypoaldosteronism, Type II Narrower
Pseudohypoaldosteronism, Type I Narrower
Hyperpotassemia and Hypertension, Familial Narrower
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