MeSH Browser

MeSH Heading: Myoclonic Cerebellar Dyssynergia
Tree Number(s): C10.228.140.252.700.250; C10.228.854.787.500; C10.574.500.825.250; C16.320.400.780.500
Unique ID: D002527
RDF Unique Identifier: http://id.nlm.nih.gov/mesh/D002527
Annotation: do not confuse entry term RAMSAY HUNT CEREBELLAR SYNDROME with RAMSAY HUNT AURICULAR SYNDROME see HERPES ZOSTER OTICUS or RAMSAY HUNT PARALYSIS SYNDROME see PARKINSONIAN DISORDERS
Scope Note: A condition marked by progressive CEREBELLAR ATAXIA combined with MYOCLONUS usually presenting in the third decade of life or later. Additional clinical features may include generalized and focal SEIZURES, spasticity, and DYSKINESIAS. Autosomal recessive and autosomal dominant patterns of inheritance have been reported. Pathologically, the dentate nucleus and brachium conjunctivum of the CEREBELLUM are atrophic, with variable involvement of the spinal cord, cerebellar cortex, and basal ganglia. (From Joynt, Clinical Neurology, 1991, Ch37, pp60-1)
Entry Term(s): Cerebellar Dyssynergia; Cerebelloparenchymal Disorder V; Dentate Cerebellar Ataxia; Dentate Cerebellar Atrophy; Dentate Nucleus Syndrome, Ramsay Hunt; Dyssynergia Cerebellaris Myoclonica; Dyssynergia Cerebellaris Myoclonica Of Hunt; Dyssynergia Cerebellaris Progressiva; Ramsay Hunt Cerebellar Syndrome; Ramsay Hunt Dentate Syndrome; Spinodentate Atrophy
Previous Indexing: Cerebellar Diseases (1966-1969)
Public MeSH Note: 2000; see CEREBELLAR DYSSYNERGIA 1991-1999; see CEREBELLAR ATAXIA 1970-1990
History Note: 2000(1970); use CEREBELLAR ATAXIA 1970-1990
Date Established: 1991/01/01
Date of Entry: 1999/01/01
Revision Date: 2012/07/03

Allowable Qualifiers: blood (BL)

cerebrospinal fluid (CF)

chemically induced (CI)

classification (CL)

complications (CO)

congenital (CN)

diagnosis (DI)

diagnostic imaging (DG)

diet therapy (DH)

drug therapy (DT)

economics (EC)

embryology (EM)

enzymology (EN)

epidemiology (EP)

ethnology (EH)

etiology (ET)

genetics (GE)

history (HI)

immunology (IM)

metabolism (ME)

microbiology (MI)

mortality (MO)

nursing (NU)

parasitology (PS)

pathology (PA)

physiopathology (PP)

prevention & control (PC)

psychology (PX)

radiotherapy (RT)

rehabilitation (RH)

surgery (SU)

therapy (TH)

urine (UR)

veterinary (VE)

virology (VI)

Nervous System Diseases [C10]
- Central Nervous System Diseases [C10.228]
  - Brain Diseases [C10.228.140]
    - Cerebellar Diseases [C10.228.140.252]
      - Spinocerebellar Degenerations [C10.228.140.252.700]
        
        Friedreich Ataxia [C10.228.140.252.700.150]
        
        Myoclonic Cerebellar Dyssynergia [C10.228.140.252.700.250]
        
        Olivopontocerebellar Atrophies [C10.228.140.252.700.650]
        
        Spinocerebellar Ataxias [C10.228.140.252.700.700]

Nervous System Diseases [C10]
- Central Nervous System Diseases [C10.228]
  - Spinal Cord Diseases [C10.228.854]
    - Spinocerebellar Degenerations [C10.228.854.787]

Nervous System Diseases [C10]
- Neurodegenerative Diseases [C10.574]
  - Heredodegenerative Disorders, Nervous System [C10.574.500]
    - Spinocerebellar Degenerations [C10.574.500.825]

Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16]
- Genetic Diseases, Inborn [C16.320]
  - Heredodegenerative Disorders, Nervous System [C16.320.400]
    - Spinocerebellar Degenerations [C16.320.400.780]

Myoclonic Cerebellar Dyssynergia Preferred

Concept UI: M0003859
Scope Note: A condition marked by progressive CEREBELLAR ATAXIA combined with MYOCLONUS usually presenting in the third decade of life or later. Additional clinical features may include generalized and focal SEIZURES, spasticity, and DYSKINESIAS. Autosomal recessive and autosomal dominant patterns of inheritance have been reported. Pathologically, the dentate nucleus and brachium conjunctivum of the CEREBELLUM are atrophic, with variable involvement of the spinal cord, cerebellar cortex, and basal ganglia. (From Joynt, Clinical Neurology, 1991, Ch37, pp60-1)
Terms: Myoclonic Cerebellar Dyssynergia Preferred Term
Term UI T364821
Date11/04/1999
LexicalTag NON
ThesaurusID NLM (2000); Dentate Cerebellar Atrophy
Term UI T369649
Date11/04/1999
LexicalTag NON
ThesaurusID NLM (2000); Dentate Nucleus Syndrome, Ramsay Hunt
Term UI T369652
Date11/04/1999
LexicalTag EPO
ThesaurusID NLM (2000); Dyssynergia Cerebellaris Myoclonica
Term UI T369650
Date11/04/1999
LexicalTag NON
ThesaurusID NLM (2000); Dyssynergia Cerebellaris Progressiva
Term UI T369653
Date11/04/1999
LexicalTag NON
ThesaurusID NLM (2000); Ramsay Hunt Cerebellar Syndrome
Term UI T007376
Date05/12/1976
LexicalTag EPO
ThesaurusID UNK (19XX); Ramsay Hunt Dentate Syndrome
Term UI T007377
Date12/26/1990
LexicalTag EPO
ThesaurusID NLM (1992); Dentate Cerebellar Ataxia
Term UI T369651
Date11/04/1999
LexicalTag NON
ThesaurusID NLM (2000); Cerebellar Dyssynergia
Term UI T007378
Date01/01/1999
LexicalTag NON
ThesaurusID NLM (1970)

Cerebelloparenchymal Disorder V Related

Myoclonic Cerebellar Dyssynergia MeSH Descriptor Data 2025