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Olivopontocerebellar Atrophies MeSH Descriptor Data 2022


MeSH Heading
Olivopontocerebellar Atrophies
Tree Number(s)
C10.177.575.550.375
C10.228.140.079.612.600
C10.228.140.252.700.650
C10.228.662.550.600
C10.228.854.787.750
C10.574.500.825.650
C16.320.400.780.750
Unique ID
D009849
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D009849
Scope Note
A group of inherited and sporadic disorders which share progressive ataxia in combination with atrophy of the CEREBELLUM; PONS; and inferior olivary nuclei. Additional clinical features may include MUSCLE RIGIDITY; NYSTAGMUS, PATHOLOGIC; RETINAL DEGENERATION; MUSCLE SPASTICITY; DEMENTIA; URINARY INCONTINENCE; and OPHTHALMOPLEGIA. The familial form has an earlier onset (second decade) and may feature spinal cord atrophy. The sporadic form tends to present in the fifth or sixth decade, and is considered a clinical subtype of MULTIPLE SYSTEM ATROPHY. (From Adams et al., Principles of Neurology, 6th ed, p1085)
Entry Version
OPCA
Entry Term(s)
Dejerine-Thomas Syndrome
Familial Olivopontocerebellar Atrophy
Inherited Olivopontocerebellar Atrophy
Nonfamilial Olivopontocerebellar Atrophy
Olivo-Ponto-Cerebellar Atrophy
Olivo-Ponto-Cerebellar Degeneration
Olivopontocerebellar Atrophy
Olivopontocerebellar Atrophy, Idiopathic
Olivopontocerebellar Degeneration
Pontoolivocerebellar Atrophy
Presenile Ataxia
Previous Indexing
Atrophy (1966-1986)
Brain Diseases (1966-1986)
Cerebellar Ataxia (1968-1986)
Cerebellar Diseases (1966-1986)
Olivary Nucleus (1966-1986)
Pons (1966-1986)
See Also
Multiple System Atrophy
Public MeSH Note
2000; see OLIVOPONTOCEREBELLAR ATROPHY 1991-1999, see SPINOCEREBELLAR DEGENERATION 1987-1990
History Note
2000(1987)
Date Established
1991/01/01
Date of Entry
1986/03/31
Revision Date
2019/05/17
Olivopontocerebellar Atrophies Preferred
Olivopontocerebellar Atrophy, Idiopathic Narrower
Familial Olivopontocerebellar Atrophy Narrower
Nonfamilial Olivopontocerebellar Atrophy Narrower
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