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Hydranencephaly MeSH Descriptor Data 2022


MeSH Heading
Hydranencephaly
Tree Number(s)
C10.500.450
C16.131.666.450
Unique ID
D006832
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D006832
Scope Note
A congenital condition where the greater portions of the cerebral hemispheres and CORPUS STRIATUM are replaced by CSF and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (Menkes, Textbook of Child Neurology, 5th ed, p307)
Entry Term(s)
Absence of Cerebral Hemispheres, Congenital
Cerebral Hemispheres, Absence, Congenital
Congenital Absence of Cerebral Hemispheres
Hemihydranencephaly
Hydranencephaly with Proliferative Vasculopathy
Public MeSH Note
91; was see under ANENCEPHALY 1979-90; was see under ANENCEPHALUS 1967-78
History Note
91(64); was see under ANENCEPHALY 1979-90; was see under ANENCEPHALUS 1967-78
Date Established
1991/01/01
Date of Entry
1999/01/01
Revision Date
2005/07/30
Hydranencephaly Preferred
Hemihydranencephaly Narrower
Hydranencephaly with Proliferative Vasculopathy Narrower
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