- Concept UI
- M0010681
- Scope Note
- A congenital condition where the greater portions of the cerebral hemispheres and CORPUS STRIATUM are replaced by CSF and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (Menkes, Textbook of Child Neurology, 5th ed, p307)
- Terms
-
Hydranencephaly
Preferred Term
Term UI
T020627
Date01/01/1999
LexicalTag
NON
ThesaurusID
NLM (1964)
-
Cerebral Hemispheres, Absence, Congenital
Term UI
T371773
Date11/03/1999
LexicalTag
NON
ThesaurusID
NLM (2000)
-
Congenital Absence of Cerebral Hemispheres
Term UI
T371775
Date11/03/1999
LexicalTag
NON
ThesaurusID
NLM (2000)
-
Absence of Cerebral Hemispheres, Congenital
Term UI
T371774
Date11/03/1999
LexicalTag
NON
ThesaurusID
NLM (2000)