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Hereditary Sensory and Autonomic Neuropathies MeSH Descriptor Data 2025


MeSH Heading
Hereditary Sensory and Autonomic Neuropathies
Tree Number(s)
C10.500.250
C10.574.500.493
C10.668.829.800.175
C16.131.666.310
C16.320.400.415
Unique ID
D009477
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D009477
Annotation
do not confuse with HEREDITARY SENSORY AND MOTOR NEUROPATHY; note entry terms for HSAN types: HSAN TYPE III see DYSAUTONOMIA, FAMILIAL is also available
Scope Note
A group of inherited disorders characterized by degeneration of dorsal root and autonomic ganglion cells, and clinically by loss of sensation and autonomic dysfunction. There are five subtypes. Type I features autosomal dominant inheritance and distal sensory involvement. Type II is characterized by autosomal inheritance and distal and proximal sensory loss. Type III is DYSAUTONOMIA, FAMILIAL. Type IV features insensitivity to pain, heat intolerance, and mental deficiency. Type V is characterized by a selective loss of pain with intact light touch and vibratory sensation. (From Joynt, Clinical Neurology, 1995, Ch51, pp142-4)
Entry Version
HEREDITARY SENSORY AUTONOMIC NEUROPATHIES
Entry Term(s)
Acroosteolysis, Giaccai Type
Acroosteolysis, Neurogenic
Congenital Insensitivity to Pain with Anhidrosis
Familial Dysautonomia, Type 2
Familial Dysautonomia, Type II
Giaccai Type Acroosteolysis
HSAN
HSAN (Hereditary Sensory Autonomic Neuropathy)
HSAN 1
HSAN 4
HSAN 5
HSAN I
HSAN IV
HSAN Type I
HSAN Type II
HSAN Type IV
HSAN Type V
HSAN V
HSAN2
HSAN5
HSANII
HSN Type I
HSN Type II
Hereditary Sensory And Autonomic Neuropathy IV
Hereditary Sensory Autonomic Neuropathy, Type 1
Hereditary Sensory Autonomic Neuropathy, Type 2
Hereditary Sensory Autonomic Neuropathy, Type 4
Hereditary Sensory Autonomic Neuropathy, Type 5
Hereditary Sensory Neuropathy Type 1
Hereditary Sensory Neuropathy Type I
Hereditary Sensory Neuropathy Type Ia
Hereditary Sensory Radicular Neuropathy
Hereditary Sensory Radicular Neuropathy, Recessive Form
Hereditary Sensory and Autonomic Neuropathy 4
Hereditary Sensory and Autonomic Neuropathy Type 1
Hereditary Sensory and Autonomic Neuropathy Type 2
Hereditary Sensory and Autonomic Neuropathy Type I
Hereditary Sensory and Autonomic Neuropathy Type II
Hereditary Sensory and Autonomic Neuropathy Type IV
Hereditary Sensory and Autonomic Neuropathy Type V
Hereditary Sensory and Autonomic Neuropathy, Type 4
Hereditary Sensory and Autonomic Neuropathy, Type 5
Insensitivity to Pain with Anhidrosis, Congenital
Insensitivity to Pain, Congenital, with Anhidrosis
Neurogenic Acroosteolysis
Neuropathies, Hereditary Sensory and Autonomic
Neuropathy Hereditary Sensory Radicular, Autosomal Dominant
Neuropathy Hereditary Sensory and Autonomic Type 1
Neuropathy, Congenital Sensory
Neuropathy, Congenital Sensory, with Anhidrosis
Neuropathy, Hereditary Sensory And Autonomic, Type I
Neuropathy, Hereditary Sensory And Autonomic, Type V
Neuropathy, Hereditary Sensory Radicular, Autosomal Dominant
Neuropathy, Hereditary Sensory Radicular, Autosomal Recessive
Neuropathy, Hereditary Sensory, Type I
Neuropathy, Progressive Sensory, Of Children
Pain Insensitivity with Anhidrosis, Congenital
Sensory Neuropathy, Hereditary
Sensory and Autonomic Neuropathies, Hereditary
Previous Indexing
Peripheral Nerve Diseases (1966-1978)
Peripheral Nerves (1966-1978)
Sensation (1966-1978)
See Also
Pain Insensitivity, Congenital
Public MeSH Note
2000; see NEUROPATHIES, HEREDITARY SENSORY AND AUTONOMIC 1989-1999; see NEUROPATHY, HEREDITARY SENSORY 1979-1988
History Note
2000(1989); use NEUROPATHY, HEREDITARY SENSORY 1979-1988
Date Established
1979/01/01
Date of Entry
1999/11/08
Revision Date
2018/06/30
Hereditary Sensory and Autonomic Neuropathies Preferred
Hereditary Sensory Radicular Neuropathy Narrower
HSAN Type IV Narrower
Hereditary Sensory and Autonomic Neuropathy Type II Narrower
Hereditary Sensory and Autonomic Neuropathy Type V Narrower
Hereditary Sensory Neuropathy Type I Narrower
Sensory Neuropathy, Hereditary Narrower
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