- Concept UI
- M0018961
- Scope Note
- A malignant tumor arising from the nuclear layer of the retina that is the most common primary tumor of the eye in children. The tumor tends to occur in early childhood or infancy and may be present at birth. The majority are sporadic, but the condition may be transmitted as an autosomal dominant trait. Histologic features include dense cellularity, small round polygonal cells, and areas of calcification and necrosis. An abnormal pupil reflex (leukokoria); NYSTAGMUS, PATHOLOGIC; STRABISMUS; and visual loss represent common clinical characteristics of this condition. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2104)
- Terms
-
Retinoblastoma
Preferred Term
Term UI
T036235
Date01/01/1999
LexicalTag
NON
ThesaurusID
-
Eye Cancer, Retinoblastoma
Term UI
T727501
Date09/25/2008
LexicalTag
NON
ThesaurusID
-
Glioblastoma, Retinal
Term UI
T036236
Date09/17/1996
LexicalTag
NON
ThesaurusID
NLM (1998)
-
Glioma, Retinal
Term UI
T036237
Date09/17/1996
LexicalTag
NON
ThesaurusID
-
Neuroblastoma, Retinal
Term UI
T036238
Date09/17/1996
LexicalTag
NON
ThesaurusID
NLM (1998)