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Caroli Disease MeSH Descriptor Data 2025


MeSH Heading
Caroli Disease
Tree Number(s)
C06.130.120.127.500
C06.198.184.500
C16.131.077.245.250
C16.131.314.184.500
C16.320.184.250
Unique ID
D016767
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D016767
Scope Note
Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION, PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.
Entry Version
CAROLI DIS
Entry Term(s)
Caroli's Disease
Caroli's Syndrome
Previous Indexing
Bile Duct Diseases/congenital (1966-1992)
Bile Ducts, Intrahepatic/abnormalities (1985-1992)
Biliary Dyskinesia (1966-1984)
Public MeSH Note
2004; see CAROLI'S DISEASE 1993-2003
History Note
2004 (1993)
Date Established
1993/01/01
Date of Entry
1992/05/07
Revision Date
2016/05/31
Caroli Disease Preferred
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