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gamma-Butyrobetaine Dioxygenase MeSH Descriptor Data 2025


MeSH Heading
gamma-Butyrobetaine Dioxygenase
Tree Number(s)
D08.811.682.690.708.401
Unique ID
D050563
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D050563
Scope Note
An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN.
Entry Term(s)
4-Trimethylaminobutyrate, 2-Oxoglutarate Oxygen Oxidoreductase (3-Hydroxylating)
Butyrobetaine Hydroxylase
Trimethylaminobutyrate Hydroxylase
gamma-Butyrobetaine Hydroxylase
gamma-Butyrobetaine, 2-Oxoglutarate Dioxygenase
gamma-Butyrobetaine,2-Oxoglutarate Dioxygenase
Registry Numbers
EC 1.14.11.1
Public MeSH Note
2006; GAMMA-BUTYROBETAINE DIOXYGENASE was indexed under MIXED FUNCTION OXYGENASES 1980-2005, KETOGLUTARIC ACID 1973-1974, BETAINE 1972-1980, BUTYRATES 1974-1979, & AMINOBUTYRIC ACID 1970-1974
History Note
2006(1980); use KETOGLUTARIC ACID 1973-1974, BETAINE 1972-1979, BUTYRATES 1974-1979, & AMINOBUTYRIC ACID 1970-1974
Date Established
2006/01/01
Date of Entry
2005/06/30
Revision Date
1955/01/01
gamma-Butyrobetaine Dioxygenase Preferred
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