- Concept UI
- M0074614
- Related Numbers
- 37255-38-2
- Scope Note
- A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase.
- Terms
-
Glutaryl-CoA Dehydrogenase
Preferred Term
Term UI
T104617
Date01/01/1955
LexicalTag
NON
ThesaurusID
NLM (2006)
-
Glutaryl CoA Dehydrogenase
Term UI
T104615
Date01/01/1955
LexicalTag
NON
ThesaurusID
NLM (2006)
-
Glutaryl-Coenzyme A Dehydrogenase
Term UI
T104616
Date01/01/1955
LexicalTag
NON
ThesaurusID
NLM (2006)