- Concept UI
- M0508347
- Scope Note
- Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown.
- Terms
-
Malignant Atrophic Papulosis
Preferred Term
Term UI
T694799
Date04/02/2007
LexicalTag
NON
ThesaurusID
-
Degos Syndrome
Term UI
T694802
Date04/02/2007
LexicalTag
EPO
ThesaurusID
-
Degos's Malignant Atrophic Papulosis
Term UI
T769467
Date04/15/2010
LexicalTag
EPO
ThesaurusID
-
Degos Disease
Term UI
T694800
Date04/02/2007
LexicalTag
EPO
ThesaurusID
-
Kohlmeier-Degos Disease
Term UI
T694801
Date04/02/2007
LexicalTag
EPO
ThesaurusID
NLM (2008)
-
Papulosis, Malignant Atrophic
Term UI
T812115
Date11/15/2011
LexicalTag
NON
ThesaurusID
OMIM (2013)
-
Erythrokeratoderma en cocardes
Term UI
T694810
Date04/02/2007
LexicalTag
NON
ThesaurusID
NLM (2008)