- Concept UI
- M000624208
- Scope Note
- A widely-expressed guanine nucleotide exchange factor protein of approximately 400 to 500 amino acids. Its N-terminal region (DENN domain) interacts with RAB GTP-BINDING PROTEINS and may regulate AUTOPHAGY, as well as PROTEIN TRANSPORT to ENDOSOMES. Expansion of the GGGGCC hexanucleotide repeat in the first intron of the C9orf72 gene is associated with FRONTOTEMPORAL DEMENTIA with AMYOTROPHIC LATERAL SCLEROSIS (FTDALS1).
- Terms
-
C9orf72 Protein
Preferred Term
Term UI
T000912418
Date11/30/2016
LexicalTag
ABX
ThesaurusID
NLM (2018)
-
Chromosome 9 Open Reading Frame 72 Protein
Term UI
T000912419
Date11/30/2016
LexicalTag
NON
ThesaurusID
NLM (2018)
-
Guanine Nucleotide Exchange Factor C9orf72
Term UI
T001108184
Date06/28/2021
LexicalTag
NON
ThesaurusID
NLM (2022)