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note specific types of Von Willebrand Disease are available
Scope Note
Group of hemorrhagic disorders in which the VON WILLEBRAND FACTOR is either quantitatively or qualitatively abnormal. They are usually inherited as an autosomal dominant trait though rare kindreds are autosomal recessive. Symptoms vary depending on severity and disease type but may include prolonged bleeding time, deficiency of factor VIII, and impaired platelet adhesion.
Entry Term(s)
Angiohemophilia
Hemophilia, Vascular
Vascular Pseudohemophilia
Von Willebrand Disorder
Von Willebrand's Factor Deficiency
von Willebrand Disease
von Willebrand Disease, Recessive Form
von Willebrand's Disease
von Willebrand's Diseases
NLM Classification #
WH 312
Public MeSH Note
2010; see VON WILLEBRAND DISEASE 1999-2009; see VON WILLEBRAND'S DISEASE 1968-1998, see HEMORRHAGIC DIATHESIS 1967, see THROMBOCYTOPATHY 1963-1966
Group of hemorrhagic disorders in which the VON WILLEBRAND FACTOR is either quantitatively or qualitatively abnormal. They are usually inherited as an autosomal dominant trait though rare kindreds are autosomal recessive. Symptoms vary depending on severity and disease type but may include prolonged bleeding time, deficiency of factor VIII, and impaired platelet adhesion.