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Beckwith-Wiedemann Syndrome MeSH Descriptor Data 2024


MeSH Heading
Beckwith-Wiedemann Syndrome
Tree Number(s)
C16.131.077.133
C16.131.260.080
C16.320.180.080
C16.320.447.375
Unique ID
D001506
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D001506
Scope Note
A syndrome of multiple defects characterized primarily by umbilical hernia (HERNIA, UMBILICAL); MACROGLOSSIA; and GIGANTISM; and secondarily by visceromegaly; HYPOGLYCEMIA; and ear abnormalities.
Entry Term(s)
EMG Syndrome
Exomphalos-Macroglossia-Gigantism Syndrome
Wiedemann Syndrome
Wiedemann-Beckwith Syndrome
Wiedemann-Beckwith Syndrome (WBS)
Previous Indexing
Abnormalities, Multiple (1968-1982)
Gigantism (1966-1982)
Hernia, Umbilical (1966-1982)
Macroglossia (1975-1982)
Tongue/abnormalities (1966-1974)
See Also
Gigantism
Silver-Russell Syndrome
Public MeSH Note
1983
History Note
1983
Date Established
1983/01/01
Date of Entry
1982/04/26
Revision Date
2023/04/14
Beckwith-Wiedemann Syndrome Preferred
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