- Concept UI
- M0374986
- Scope Note
- An autosomal dominant disorder with an acronym of its seven features (LENTIGO; ELECTROCARDIOGRAM abnormalities; ocular HYPERTELORISM; PULMONARY STENOSIS; abnormal genitalia; retardation of growth; and DEAFNESS or SENSORINEURAL HEARING LOSS). This syndrome is caused by mutations of PTPN11 gene encoding the non-receptor PROTEIN TYROSINE PHOSPHATASE, type 11, and is an allelic to NOONAN SYNDROME. Features of LEOPARD syndrome overlap with those of NEUROFIBROMATOSIS 1 which is caused by mutations in the NEUROFIBROMATOSIS 1 GENES.
- Terms
-
LEOPARD Syndrome
Preferred Term
Term UI
T431506
Date12/20/2000
LexicalTag
ACX
ThesaurusID
-
Multiple Lentigines Syndrome
Term UI
T532190
Date02/06/2003
LexicalTag
NON
ThesaurusID
-
Lentiginosis Cardiomyopathic
Term UI
T825009
Date06/26/2012
LexicalTag
NON
ThesaurusID
OMIM (2013)
-
Cardiomyopathic Lentiginosis
Term UI
T834016
Date12/10/2012
LexicalTag
NON
ThesaurusID
ORD (2010)
-
Cardio-Cutaneous Syndrome
Term UI
T842084
Date04/18/2013
LexicalTag
NON
ThesaurusID
GHR (2014)
-
Noonan Syndrome with Multiple Lentigines
Term UI
T842086
Date04/18/2013
LexicalTag
EPO
ThesaurusID
GHR (2014)
-
Progressive Cardiomyopathic Lentiginosis
Term UI
T842087
Date04/18/2013
LexicalTag
NON
ThesaurusID
GHR (2014)