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Isolated Noncompaction of the Ventricular Myocardium MeSH Descriptor Data 2022


MeSH Heading
Isolated Noncompaction of the Ventricular Myocardium
Tree Number(s)
C14.240.400.660
C14.280.238.281.500
C14.280.400.660
C16.131.077.477
C16.131.240.400.655
C16.320.322.370
Unique ID
D056830
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D056830
Scope Note
Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen.
Entry Term(s)
Isolated Non-compaction of the Ventricular Myocardium
Isolated Noncompaction of the Left Ventricular Myocardium, X-Linked
Noncompaction of the Left Ventricular Myocardium, Autosomal Dominant
Public MeSH Note
2010
History Note
2010
Date Established
2010/01/01
Date of Entry
2009/07/06
Isolated Noncompaction of the Ventricular Myocardium Preferred
Noncompaction of the Left Ventricular Myocardium, Autosomal Dominant Narrower
Isolated Noncompaction of the Left Ventricular Myocardium, X-Linked Narrower
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