- Concept UI
- M0017748
- Scope Note
- A 53-kDa protein that is a positive regulator of the alternate pathway of complement activation (COMPLEMENT ACTIVATION PATHWAY, ALTERNATIVE). It stabilizes the ALTERNATIVE PATHWAY C3 CONVERTASE (C3bBb) and protects it from rapid inactivation, thus facilitating the cascade of COMPLEMENT ACTIVATION and the formation of MEMBRANE ATTACK COMPLEX. Individuals with mutation in the PFC gene exhibit properdin deficiency and have a high susceptibility to infections.
- Terms
-
Properdin
Preferred Term
Term UI
T033682
Date01/01/1999
LexicalTag
NON
ThesaurusID
NLM (1966)
-
Complement Factor P
Term UI
T033683
Date09/12/1997
LexicalTag
NON
ThesaurusID
NLM (1999)